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Case report: interrupted aortic arch

  • Petrus Sewe Pajo ,
  • Dewa Gde Mahiswara Suadiatmika ,
  • Elysanti Dwi Martadiani ,

Abstract

Introduction: Interrupted aortic arch (IAA) is one of the congenital heart diseases characterized by a complete anatomical and luminal disruption between the ascending and descending aorta. It is frequently accompanied by other congenital heart defects, such as PDA and VSD. IAA in adults is exceptionally rare. The presence of collateral circulation and PDA are key factors for patient survival. Thorax CTA is an excellent modality for imaging and diagnosis, ensuring that appropriate treatment can be carried out.

Case Presentation: An 18-year-old male patient presented with complaints of worsening shortness of breath 10 days prior to the examination. The shortness of breath has been experienced since school age, often occurring during exercise and strenuous activity. Thorax CTA results indicated IAA type A subtype 1 according to Celoria and Patton classification, PDA type A according to Krichenko classification, perimembranous VSD, cardiomegaly, and pulmonary hypertension.

Conclusion: IAA in adults is exceptionally rare. Adult IAA patients may exhibit no symptoms or may present with symptoms of CHF. Thorax CTA is one of the modalities employed to confirm the diagnosis of IAA. It can visualize the interruption and separation between the ascending and descending aorta, as well as the associated anomalies. The presence of a PDA and VSD ensures that the descending thoracic aorta distal to the defect continues to receive some oxygenated blood from the heart. Thorax CTA plays a pivotal role in establishing cases of IAA, as it helps clinicians to make a quick and accurate diagnosis.

References

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How to Cite

Pajo, P. S. ., Suadiatmika, D. G. M. ., & Martadiani, E. D. . (2023). Case report: interrupted aortic arch. Intisari Sains Medis, 14(3), 1240–1244. https://doi.org/10.15562/ism.v14i3.1888

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Petrus Sewe Pajo
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ISM Journal


Dewa Gde Mahiswara Suadiatmika
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Elysanti Dwi Martadiani
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ISM Journal