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Choledochal Cyst (CC) Todani type I in two years old girl: a case report

Abstract

Backgrounds: Choledocal cyst (CC) is a rare congenital cystic dilation of the bile duct and can be associated with severe complications, including malignancy and inflammation of the surrounding anatomy. Approximately 80% of CC is diagnosed in infants and young children in the first decade of life. Complete surgical resection is recommended in patients with choledochal malformations with excellent outcomes. 

Case Presentation: A two-year-old girl had intermittent abdominal pain in the upper right quadrant. This complaint was accompanied by fever, nausea and vomiting, decreased appetite and drinking. The physical examination revealed jaundice on the sclera and palpable liver, two fingers below the costal arch. Abdominal ultrasound revealed a cystic mass in the right lower lobe suggestive of the hepatic cyst with inflammation of the cystic head of the pancreas and minimal free fluid per lumen. An abdominal C.T. scan without contrast showed a choledochal cyst classified as Todani Type IV. A cyst in the bile duct was found during the surgical procedure 

Conclusion: Choledocal cyst is one of the differential diagnoses in children with symptoms of abdominal pain. Appropriate surgical measures should be undertaken to avoid complications.

References

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How to Cite

Dira, I. K. P. A., Putra, I. G. N. S., Karyana, I. P. G., Nesa, N. N. M., Ariyanta, K. D., & Dharmajaya, I. M. (2023). Choledochal Cyst (CC) Todani type I in two years old girl: a case report. Intisari Sains Medis, 14(3), 1124–1129. https://doi.org/10.15562/ism.v14i3.1839

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I Komang Prayoga Ariguna Dira
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I Gusti Ngurah Sanjaya Putra
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I Putu Gede Karyana
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Ni Nyoman Metriani Nesa
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Kadek Deddy Ariyanta
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